Pocket Pediatrics: The Massachusetts General Hospital for Children Handbook of Pediatrics (Pocket Notebook Series), 2 Ed.

HYPOPHOSPHATEMIA/HYPERPHOSPHATEMIA

(Lancet 1998;352:391)

Definition: Nml serum [Phos] 2.8–4.5 mg/dL w/ slightly ↑ concentration in children vs. adults.

Pathophysiology

• Homeostasis by balance btw GI absorption (60–80% dietary Phos absorbed) and renal excretion (80% Phos reabsorbed in proximal tubule, coupled to Na)

• Controlled by PTH (inc renal secretion) and vit D (inc GI absorp, dec urine excretion)

Hypophosphatemia

Etiology

• ↑ urinary excretion: HyperPTH, vit D deficiency, renal tubule defects (Fanconi, hereditary hypophosphatemic rickets [formerly known as vit D dependent rickets] caused by mutations in PHEX [X-linked], FGF23 [autosomal dominant], DMP1 [autosomal recessive], SLC34A3 [autosomal recessive hypophosphatemic rickets with hypercalciuria] etc.), metab or resp acidosis, acetazolamide (Nat Rev Nephrol 2010;6:657; Curr Opin Pediatr 2007;19:488)

• ↓ intestinal absorption: Dietary restriction, chronic antacid use, vit D def, chronic diarrhea, steatorrhea

• Internal redistribution: Hungry bone syndrome, respiratory alkalosis, recovery from DKA or malnutrition, refeeding syndrome (Pediatr Clin N Am 2009;56:1201), sepsis

Clinical manifestations

• Rarely symptomatic unless severe (<1 mg/dL); generally due to ATP deficiency

• Muscle dysfunction w/ prox myopathy, dysphagia, and ileus; rarely rhabdo

• Respiratory failure 2/2 weakness of respiratory muscles

• Cardiac involvement w/ impaired contractility and CHF

• Heme abnormalities w/ hemolysis, thrombocytopenia, and impaired phagocytosis

• Renal dysfunction w/ calcium and magnesium wasting

• Neurologic dysfxn w/ metab encephalopathy, seizures, lethargy, confusion, coma

Evaluation: Chem 7, Ca (iCa), Phos, Mg, vit D, PTH, UCa, UPhos, UCr, and urine pH

Management

• Acute onset w/ severe depletion (<1 mg/dL) and/or symptoms treat w/ IV

• KPhos contains 4.4 mEq K+ and 3 mMol phosphate/mL. NaPhos contains 4 mEq Na+ and 3 mMol phosphate/mL

• Administer 0.1–0.2 mMol/kg phosphate over 6 hr, then maintenance infusion 15–45 mg/kg/d; observe for HypoCa and follow [Ca] × [Phos] product

• Chronic onset: NeutraPhos contains 250 mg (= 8 mMol) phosphate per packet, half as the Na salt and half as the K salt

• Cow’s milk has 1 mg Phos/mL

Hyperphosphatemia

Etiology

• Inc exogenous load: Cow’s milk intake in infants, vit D intoxication, phosphate containing enemas, supplements

• Inc endogenous load: Tumor lysis syndrome, rhabdomyolysis, malignant hyperthermia (w/ anesthesia), hemolysis, acidosis

• Dec renal excretion: Renal failure, hypoPTH, Mg def, acromegaly, thyrotoxicosis

Clinical manifestations

• Rapid increase in [Phos] can result in hypoCa and assoc symptoms

• [Ca] × [Phos] >70 results in soft-tissue deposition of calcium

Evaluation: Serum electrolytes, BUN/Cr, Ca (iCa), Phos, Mg, vit D, PTH, ABG, UCa, UPhos, UCr, and urine pH

Management

Most effective therapy is reduction of intestinal absorption 2/2 dec dietary intake and use of phosphate binders (calcium carbonate, calcium acetate [PhosLo], Renagel [binding resin])

• If 2/2 cell lysis, management as per management of tumor lysis syndrome or rhabdomyolysis (IV fluid, consider mannitol)

• If severe symptoms and 2/2 renal failure, consider dialysis



If you find an error or have any questions, please email us at admin@doctorlib.org. Thank you!